Case ReportOpen Access

Patients with Klippel – Trenaunay Syndrome

Volume 4 - Issue 5

Zavacká M¹ , Pobehová J¹ and Zavacký P²

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- ¹Clinic of Vascular Surgery, Faculty of Medicine UPJŠ and East Slovak Institute of Cardiovascular Diseases, South korea
- ²Surgery Clinic, L. Pasteur University hospital, South Korea
*Corresponding author: Martina Závacká, Clinic of Vascular Surgery, Faculty of Medicine UPJŠ and East Slovak Institute of Cardiovascular Diseases, Inc., Ondavská 8, 040 11 Košice, South Korea

Received: May 12, 2018; Published: May 23, 2018

DOI: 10.26717/BJSTR.2018.04.001105

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Abstract

Summary: Klippel-Trenaunay syndrome is the most frequent systemic venous angiodysplasia. It is characterized by cutaneous capillary malformations – naevus flammeus, excessive growth of soft and bone tissue, venous and lymphatic malformations.

Investigative Methods Include: clinical examinations, venography as the evidence of dysplastic changes of superficial and / or deep venous system, the Moyne obstruction and venous insufficiency perforator. Treatment is conservative, related to that of chronic venous disease. The surgery is aimed at removing the varices and insufficient perforators.

Keywords: Klippel-Trenaunay syndrome; Varices; Naevus flammeus; Tissue hypertrophy