*Corresponding author:
Cássio Daniel Araújo da Silva, National Institute of Women, Child and Adolescent Health Fernandes Figueira- IFF/Fiocruz Rio de Janeiro, BrazilReceived: January 20, 2018; Published: January 31, 2018
DOI: 10.26717/BJSTR.2018.02.000712
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Cystic Fibrosis (CF) is a multisystem genetic disease whose main cause of morbidity and mortality is progressive impairment of lung function associated with loss of quality of life and functional capacity. We report the clinical case of an 18-year-old adolescent accompanied at a reference center with bronchial hyper-secretion, recurrent infections, bacterial colonization, important obstructive ventilatory disorder, and pulmonary computed tomography (CT) showing a heterogeneous pattern. The authors emphasize the importance of continuous monitoring of pulmonary, nutritional and functional parameters, allowing for more effective early interventions.
Key words: Cystic Fibrosis; Lung Diseases; Evaluation; Follow-up
Abbreviations: CF: Cystic Fibrosis; CFTR: Cystic Fibrosis Trans-membrane Conductance Regulator; PA: Pseudomonas Aeruginosa; FEV1: Forced Expiratory Volume at Firs second; FVC: Forced Vital Capacity; ADL: Activities of Daily Living; 6MWT: Six-Minute Walk Test
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